【2025年】研究成果

書籍

 著者氏名  論文タイトル名 書籍全体の編集者名書籍名出版社名出版地ページ
中尾遼平, 松松井尚子, 和和泉唯信 Stiff person症候群 亀山 隆 脊椎脊髄ジャーナル 三輪書店 東京 747-753 

雑誌

 発表者氏名  論文タイトル名

 発表誌名  

巻号ページ
Matsui N, Tanaka K, Kokubun N,  Hatanaka Y , Ishida M ,  Osaki Y ,  Watanabe T, Watanabe O ,  Matsuura E ,  Takashima H ,  Sato Y, Kuwabara S, Izumi YPrevalence, clinical profiles, and prognosis of Isaacs syndrome: A nationwide survey study in Japan. Neurol Sci                                                       
472    123442                                       
Zhang X, Kira JI, Yokote A, Sakoda A, Yamashita KI, Mitsuishi M, Ogata H, Tashiro T, Isobe N, Sato R, Kanda T, Ide T, Koike H, Mishima T, Tsuboi Y, Kobayashi M, Kitagawa K, Namihira Y, Ohya Y, Fukata Y, Fukata M, Imamura T, Maimaitijiang G, Nakamura Y.Clinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody-Positive Autoimmune Nodopathy. Neurol Neuroimmunol Neuroinflamm. 12    e200504                                                
Tashiro T, Ogata H, Fukami Y, Maimaitijiang G, Hayashida H, Deguchi K, Hamada Y, Ito Y, Kanai M, Katsumoto A, Kishi R, Koga M, Kurokawa T, Machida A, Mihara M, Miyaue N, Mori Y, Naba I, Nakae Y, Nakamura A, Nishimura H, Okamoto T, Saji E, Satake R, Sekiguchi K, Shibuya M, Shimoda M, Shimohata T, Takeda Y, Taneda K, Tezuka T, Togo M, Uehara T, Yamaguchi K, Yoshikura N, Yamasaki R, Kira JI, Koike H, Katsuno M, Isobe N. Clinical, Electrophysiologic, and Pathologic Features of Anti-Contactin-Associated Protein 1 Autoimmune Nodopathy. Neurology. 105 e214143   
Inoue Y, Fujii T, Kashu KY, Watanabe M, Masaki K, Tanaka E, Kira YI, Takeuchi H, Yamaura K, Isobe N.  Associations between serum levels of alpha-calcitonin gene-related peptide and clinical features of neuromyelitis optica spectrum disorders. J Neuroimmunol. 404 578615 
Onishi Y, Uzawa A, Yasuda M, Akamine H, Ogaya E, Handa H, Ozawa Y, Kuwabara S.  Elevated serum levels of IL-10 family and IL-12 family cytokines in myasthenia gravis. Neuroimmunol 404 578621
Uzawa A, Akamine H, Yasuda M, Handa H, Ogaya E, Kurumada K, Onishi Y, Kuwabara S The Fusion Protein MuSK-Fc Functions as a Decoy to Block the Binding of Anti-MuSK Antibodies to MuSK.Scand J Immunol.  101e70033 
Onishi Y, Uzawa A, Yasuda M, Akamine H, Ogaya E, Handa H, Ozawa Y, Kuwabara S. Elevated serum levels of IL-10 family and IL-12 family cytokines in myasthenia gravis.  J Neuroimmunol.  404 578621 
Akamine H, Uzawa A, Kuwabara S, Suzuki S, Onishi Y, Yasuda M, Ozawa Y, Kawaguchi N, Kubota T, Takahashi MP, Suzuki Y, Watanabe G, Kimura T, Sugimoto T, Samukawa M, Minami N, Masuda M, Konno S, Nagane Y, Utsugisawa K. Predicting achievement of clinical goals using machine learning in myasthenia gravis. PLoS One.20 e0330044 
Akamine H, Uzawa A, Kuwabara S, Suzuki S, Onishi Y, Yasuda M, Ozawa Y, Kawaguchi N, Kubota T, P Takahashi M, Suzuki Y, Watanabe G, Kimura T, Sugimoto T, Samukawa M, Minami N, Masuda M, Konno S, Nagane Y, Utsugisawa K. Association between Myasthenia Gravis and Smoking. Intern Med.64(24) 3478-3485 
Uzawa A, Suzuki S, Kuwabara S, Yasuda M, Akamine H, Onishi Y, Ozawa Y, Kawaguchi N, Kubota T, Takahashi MP, Suzuki Y, Watanabe G, Kimura T, Sugimoto T, Samukawa M, Minami N, Masuda M, Konno S, Nagane Y, Utsugisawa K. Corticosteroid-induced Cushingoid Appearance in Myasthenia Gravis. Intern Med.64 3486-3492 
Nakajima A, Yanagimura F, Saji E, Shimizu H, Toyoshima Y, Yanagawa K,  Arakawa M, Yokoseki A, Wakasugi T, Okamoto K, Watanabe K, Minato K, Otsu Y, Nozawa Y, Kobayashi D, Sanpei K, Kikuchi H, Hirohata S, Awamori K, Nawata A, Yamada M, Takahashi H, Nishizawa M, Igarashi H, Sato N, Kakita A, Onodera O, Kawachi I. Long-term clinical landscapes of spinal hypertrophic pachymeningitis with anti-neutrophil cytoplasmic antibody-associated vasculitis. Neurology 104(8) e213420
Onishi Y, Uzawa A, Yasuda M, Akamine H, Ogaya E, Handa H, Ozawa Y, Kuwabara S.  Elevated serum levels of IL-10 family and IL-12 family cytokines in myasthenia gravis.J Neuroimmunol.  404 578621 
Yamamura T, Isobe N, Kawachi I, Nohara C, Miyazaki Y, Tomita M, Kamei Y, Yamashita K, Nakahara J, Nakashima I, Fujihara K.  Safety and Effectiveness of Satralizumab in Japanese Patients with Neuromyelitis Optica Spectrum Disorder: A 30Month Interim Analysis of Postmarketing Surveillance. Neurol Ther.  14  2429-2451  
Yanagimura F, Nakajima A, Saji E, Kawachi I NMOSD: innate immunology revisited Clinical and Experimental Neuroimmunology 16(4) 301-309
Tanaka K, Yoshikawa M, Inoue Y, Tsumura K, Hoshino Y, Shichijo C, Ide T, Suzuyama K, Koike H Efgartigimod Successfully Ameliorated Acute Exacerbation of Myasthenia Gravis with Anti-muscle-specific Kinase Antibodies Intern Med 64(6) 925-929 
Yoshikawa M, Inoue Y, Tanaka K, Tsumura K, Hoshino Y, Shichijo C, Ide T, Suzuyama K, Iwasaki M, Eriguchi M, Yukitake M, Takashima H, Koike H.  Real-World Experience with FcRn Inhibitors Efgartigimod and Rozanolixizumab in Myasthenia Gravis: Administration in Multiple Cycles and Transition from Intravenous to Subcutaneous Formulation. Neurol Ther 14(3) 977-988
Matsui N, Tanaka K, Kokubun N, Hatanaka Y, Ishida M, Osaki Y, Watanabe T, Watanabe O, Matsuura E, Takashima H, Sato Y, Kuwabara S, Izumi Y; Japanese Isaacs study group. Prevalence, clinical profiles, and prognosis of Isaacs syndrome: A nationwide survey study in Japan.  J Neurol Sci. 472 123442 
Maeda Y, Ikeguchi R, Masui K,Kurata A, Kitagawa K,Shimizu YAnti‐neutrophil cytoplasmic antibody‐associated central nervous system vasculitis mimicking brain tumor: A case report Neuropathology 2025; 45, 135–13945135-139
Ikeguchi R, Shimizu Y, Kuroda R, Todo K.Progress in theTreatment of Neuromyelitis Optica Spectrum Disorder: From Pathogenic Insights to Biologics Intern Med. -103:106706. doi:10.1016/
Ikeguchi R, Shimizu Y, Todo K. Progress in theTreatment of Neuromyelitis Optica Spectrum Disorder: From Pathogenic Insights to Biologics Intern Med. -doi: 10.2169/internalmedicine.6772-25 
Ishii M, Arai S, Ikeguchi R, Shimizu Y, Todo K. Hydrocephalus as an Initial Presentation of Myelin Oligodendrocyte Glycoprotein (MOG) Antibody-Associated Disease: A Case Report and Review of Tumor-Mimicking Demyelination Cureus. 17 e89246 
Shimizu Y,  Ikeguchi R, Fujihara K, Todo K. Progress in the management of pregnancy in patients with neuromyelitis optica spectrum disorder. Ther Adv Neurol Disord. -18:17562864251384504
Maeda Y, Ikeguchi R, Masui K, Kurata A, Kitagawa K, Shimizu Y.  Anti-neutrophil cytoplasmic antibody-associated central nervous system vasculitis mimicking brain tumor: A case report. Neuropathology. 45 135-139
Tahara M, Awaya, T Saito K, and  Sawada HLong-term suppression of relapses by dimethyl fumarate in a relapsing pediatric patient with myelin oligodendrocyte glycoprotein antibody–associated disease manifesting as acute disseminated encephalomyelitis, unilateral optic neuritis, and seizure episodes Front Immunol. 161551379
Komiya H, Takeuchi H, Ogasawara A, Ogawa Y, Kubota S, Hashiguchi S, Takahashi K, Kunii M, Tanaka K, Tada M, Doi H, Tanaka F Siponimod inhibits microglial inflammasome activation Neurosci Res 213138-145
Muryoi A, Nei M, Fujimori J, Nakashima I Clinical value of the Japanese version of patient-reported multiple sclerosis neuropsychological screening questionnaire. Clin Exp Neuroimmunol -doi:10.1111/cen3.12829
Shibuya R, Ishikuro K, Hattori N, Takasawa S、Hirosawa H, Yamamoto M, Konishi H, Nakane S, Noguchi K, Nakatsuji Y.  Effects of transcranial direct current stimulation on multiplesclerosis and neuromyelitis optica spectrum disorder: Adouble-blind, randomized, crossover trial Clin Exp Neuroimmun16 348–356
Nomura T, Niino M, et al. Interleukin-6 Immunology in Macrophage Activation Syndrome Related to Neuroimmunological Diseases. Intern Med64(6)941-945
Kanbayashi T, Kamiya H, Oishi C, Tsukamoto H, Hatanaka Y, Kobayashi S, Sonoo M. Utility of the combination of median nerve SEPs and auditory brainstem responses for diagnosing Bickerstaff brainstem encephalitis. Clin Neurophysiol 176 2110766 
Shimizu Y, Ikeguchi R, Fujihara K, Todo K Progress in the Management of Pregnancy in Patients with Neuromyelitis Optica Spectrum Disorder Ther Adv Neurol Disord 18 17562864251384504 
Suichi T, Misawa S, Shibuya K, Morooka M, Ogushi M, Oshima-Hasegawa N, Tsukamoto S, Takeda Y, Mimura N, Sakaida E and  Kuwabara S Daratumumab (anti-CD38)- and elotuzumab (anti-SLAMF7)-based treatments for refractory POEMS syndrome: a single-center case series Hematology -2519896 
Yoshikawa H, Adachi Y, Nakamura Y, Kuriyama N, Murai H, Nomura Y, Sakai Y, Iwasa K, Furukawa Y, Matsui M, Kuwabara S. Comparative study of Japanese nationwide epidemiological studies of myasthenia gravis using datasets of 2006 and 2018. PLoS One 20(10) e0334041
Doi:10.1371/journal.pone.0334041